Gradually increasing atrophy of all tissue structures of half of the face, then of the neck, and sometimes other parts of the half of the body.
Etiology and pathogenesis of progressive atrophy of the face
The nature of the disease has not yet been disclosed, it is assumed that the centers of the autonomic nervous system are affected. The disease can be hereditary-family in nature.
Clinic of Progressive Face Atrophy
The disease first appears in young years and, gradually progressing, leads to a sharp asymmetry of the face due to atrophy of one half. Women suffer more often. In advanced cases, the diagnosis is not difficult. At the beginning of the disease, they resort to various tests to establish the degree of functional activity of the autonomic nervous system on the corresponding side of the face.
Treatment of progressive facial atrophy
The treatment is symptomatic, in the early stages it is aimed at reducing the pathological activity of the peripheral parts of the sympathetic system mainly in the area of the stellate node. To eliminate the developed asymmetry, recovery operations are performed.
Atrophy of the face unilateral progressive
Unilateral progressive atrophy of the face ( hemiatrophia facialis progressiva , Romberg syndrome , facial trophoneurosis, lamellar aplasia). It is rare. More common in children and adults.
Etiology and pathogenesis of unilateral progressive facial atrophy
Little studied. Indicate the defeat of the trigeminal nerve, sympathetic or parasympathetic system, disorders of the endocrine system, post-traumatic consequences, infectious diseases.
Unilateral progressive facial atrophy clinic
Unilaterally in the cheek area, near the eye, cheekbones, lower jaw, bluish-dark or normal skin color spots appear, which increase. Atrophy of all layers of the skin and underlying tissues (muscles, bones) occurs. There is no sweat in the foci – and salivation , hair falls out. Neuralgic pains and disturbances of sensitivity ( hypo – and hypersthesia ) may disturb . The process extends to the corresponding half of the sky, palatine curtain, tongue. It ends with an asymmetric face (the affected half is less than healthy, the skin is atrophied, folded). It can be combined with scleroderma and acrodermatitis .